scispace - formally typeset
M

Marian DiFiglia

Researcher at Harvard University

Publications -  183
Citations -  25514

Marian DiFiglia is an academic researcher from Harvard University. The author has contributed to research in topics: Huntingtin & Huntingtin Protein. The author has an hindex of 72, co-authored 175 publications receiving 23627 citations. Previous affiliations of Marian DiFiglia include University of Massachusetts Medical School & University of Massachusetts Amherst.

Papers
More filters
Journal ArticleDOI

Aggregation of Huntingtin in Neuronal Intranuclear Inclusions and Dystrophic Neurites in Brain

TL;DR: An NH2-terminal fragment of mutant huntingtin was localized to neuronal intranuclear inclusions and dystrophic neurites in the HD cortex and striatum, and polyglutamine length influenced the extent of huntingtin accumulation in these structures.
Journal ArticleDOI

Guidelines for the use and interpretation of assays for monitoring autophagy in higher eukaryotes

Daniel J. Klionsky, +235 more
- 16 Feb 2008 - 
TL;DR: A set of guidelines for the selection and interpretation of the methods that can be used by investigators who are attempting to examine macroautophagy and related processes, as well as by reviewers who need to provide realistic and reasonable critiques of papers that investigate these processes are presented.
Journal ArticleDOI

Formation of neuronal intranuclear inclusions underlies the neurological dysfunction in mice transgenic for the hd mutation

TL;DR: In this paper, the authors observed that mice transgenic for exon 1 of the human HD gene carrying (CAG)115 to 157 repeat expansions develop pronounced neuronal intranuclear inclusions, containing the proteins huntingtin and ubiquitin, prior to developing a neurological phenotype.
Journal ArticleDOI

Huntingtin is a cytoplasmic protein associated with vesicles in human and rat brain neurons.

TL;DR: Immunohistochemistry in human and rat brain revealed widespread cytoplasmic labeling of huntingtin within neurons, rather than the more selective pattern of axon terminal labeling characteristic of many vesicle-associated proteins.
Journal ArticleDOI

Evidence for degenerative and regenerative changes in neostriatal spiny neurons in Huntington's disease

TL;DR: The findings provide evidence for simultaneous degeneration and growth of spiny neurons in Huntington's disease and support the view that a specific population of neostriatal neurons is selectively involved in its pathogenesis.